This category includes disorders caused by prions, which are infectious proteins. Examples of the transmissible spongiform encephalopathies they cause include Creutzfeldt-Jakob Syndrome, Bovine Spongiform Encephalopathy, Gerstmann-Straussler-Scheinker Disease, Kuru, Scrapie in sheep and goats, Chronic Wasting Disease of cervids, Transmissible Mink Encephalopathy, and Fatal Familial Insomnia.
Subcategories 1
Related categories 5
Sites 6
- Protein Misfolding in Prion Disease Includes review of the pathogenesis of prion diseases.
- Prion propagation in vitro: are we there yet? Analysis of prion disease progression in cellular and animal models.
- Kuru Information Page Compiled by the National Institute of Neurological Disorders and Stroke (NINDS).
- The Prion Protein Knockout Mouse Paper by Andrew D Steele, Susan Lindquist and Adriano Aguzzi discussing the many phenotypes.
- Molecular Evolution of Prions Article about the different evolutionary pathways of bovids and humans.
- 3D Structure of Prion Protein Technical explanation of sheep and human prion proteins in normal and dimer forms.